Anorectal manometry. In this test, a small tube is
inserted into the rectum to measure how well the muscles in the anus are
working. If the muscles don't relax, it can sometimes be a sign of Hirschsprung's disease.
How is it treated?
Children with Hirschsprung's
disease need surgery to remove the diseased part of the large intestine.
Surgery is often done within the first days or month of life, soon after the
disease is found. Treatment may involve one or two
The first surgery removes the damaged part of the intestine and may create a colostomy or ileostomy so that the intestine can heal. (With an ostomy, stool leaves the body through an opening in the belly and collects in a bag.)
If your baby gets an ostomy during the first surgery (not all babies do), a second surgery will be done to close the ostomy. This will allow stool to pass through the body normally again.
Most babies are in the hospital from a couple of days up to 1 week. Being involved in your baby's care while he or she is in the hospital may help you feel more comfortable when you take your baby home. Talk with the doctor about how to feed and care for your baby at home, and make sure you know what problems to watch for. It's normal to feel nervous, but don't be afraid to hold and handle your baby.
Some children have long-term (chronic) problems with stomachaches and
bowel problems after surgery. But most of the time, these problems
aren't severe. Depending on the problem, there are a number of treatment
options. These include medicine,
cognitive-behavioral therapy, and more surgery.
In a few cases, emergency surgery may be needed if a dangerous problem
such as serious swelling of the small and large intestines (enterocolitis)
Health Tools help you make wise health decisions or take action to improve your health.
Actionsets are designed to help people take an active role in managing a health condition.
International Foundation for Functional Gastrointestinal
P.O. Box 170864
Milwaukee, WI 53217-8076
The International Foundation for Functional
Gastrointestinal Disorders (IFFGD) is a nonprofit organization that provides
information and support to adults and children affected by hard-to-diagnose
gastrointestinal (GI) disorders. The website has information about GI symptoms
and conditions such as irritable bowel syndrome, indigestion, gastroesophageal
reflux disease (GERD), incontinence, gas, bloating, belching, heartburn,
nausea, and belly pain.
March of Dimes
1275 Mamaroneck Avenue
White Plains, NY 10605
The March of Dimes tries to improve the health of babies
by preventing birth defects, premature birth, and early death. March of Dimes
supports research, community services, education, and advocacy to save babies'
lives. The organization's website has information on premature birth, birth
defects, birth defects testing, pregnancy, and prenatal care.
National Digestive Diseases Information Clearinghouse
2 Information Way
Bethesda, MD 20892-3570
This clearinghouse is a service of the U.S. National
Institute of Diabetes and Digestive and Kidney Diseases (NIDDK), part of the
U.S. National Institutes of Health. The clearinghouse answers questions;
develops, reviews, and sends out publications; and coordinates information
resources about digestive diseases. Publications produced by the clearinghouse
are reviewed carefully for scientific accuracy, content, and readability.
North American Society for Pediatric Gastroenterology,
Hepatology, and Nutrition (NASPGHAN)
P.O. Box 6
Flourtown, PA 19031
NASPGHAN promotes advances in clinical care, research,
and education for infants, children, and teens with digestive disorders. The
family resources page of this Web site has information about pain in the belly,
diarrhea, constipation, vomiting, poor weight gain, nutritional problems, and
diseases of the liver, bowel, and pancreas.
Vanderhoof JA, Young RJ (2006). Hirschsprung disease. In FD Burg et al., eds., Current Pediatric Therapy, 18th ed., pp. 529–532. Philadelphia: Saunders Elsevier.
Other Works Consulted
Constipation Guideline Committee (2006). Evaluation and treatment of constipation in infants and children: Recommendations of the North American Society for Pediatric Gastroenterology, Hepatology and Nutrition. Journal of Pediatric Gastroenterology and Nutrition, 43(3), pp. e1–e13. Also available online: http://www.naspghan.org/wmspage.cfm?parm1=295.
Fiorino KN, et al. (2011). Motility disorders and Hirschsprung disease. In RM Kliegman et al., eds., Nelson Textbook of Pediatrics, 19th ed., pp. 1283–1287. Philadelphia: Saunders.
Gomez J, Parkman HP (2009). Megacolon section of Gastrointestinal motility and functional disorders. In EG Nabel, ed., ACP Medicine, section 4, chap. 14. Hamilton, ON: BC Decker.
Kahn E, Daum F (2010). Enteric nervous system section of Anatomy, histology, embryology, and developmental anomalies of the small and large intestine. In M Feldman et al., eds., Sleisenger and Fordtran's Gastrointestinal and Liver Disease, 9th ed., vol. 2, pp. 1636–1641. Philadelphia: Saunders.
Sood MR, Calkins CM (2011). Motor disorders of the stomach, small bowel, and colon. In CD Rudolph et al., eds., Rudolph's Pediatrics, 22nd ed., pp. 1433–1437. New York: McGraw-Hill.
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